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Glutaryyli-KoA-dehydrogenaasi
Hierarki: | |
Bredare villkor: | |
Anmärkning: | Acyl Coenzyme A (1973-1979) | Coenzymes (1973-1979) | Glutarates (1973-1980) | Oxidoreductases (1983-2003) | Oxidoreductases Acting on CH-CH Group Donors (2004-2005)X |
Anmärkning: | A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase.
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historyNote*: | 2006(1973)
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publicMeSHNote*: | 2006; GLUTARYL-COA DEHYDROGENASE was indexed under ACYL COENZYME A 1973-1979; under GLUTARATES 1973-1982; and under COENZYME A 1973-1979; under OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS 2004-2005
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activeMeSHYear*: | |
dateCreated*: | 2005-06-30X |
dateEstablished*: | 2006-01-01X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | AKEX |
recordOriginator*: | AKEX |
Typ: | |
Samordna villkor: | |
URI: | |
Termer och motsvarande begrepp: | Glutaryl-CoA Dehydrogenase (en) XGlutaryl-Coenzyme A Dehydrogenase (en, ersatt) Glutaryl CoA Dehydrogenase (en, ersatt) |
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