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Iktyos, lamellär
Hierarki: | ∟ ∟ ∟ ∟ ∟ ∟ Iktyos, lamellär 1 sidobegrepp∟ ∟ ∟ ∟ ∟ Iktyos, lamellär 1 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ Iktyos, lamellär 1 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ Iktyos, lamellär 1 sidobegrepp∟ ∟ ∟ ∟ ∟ Iktyos, lamellär 1 sidobegrepp∟ ∟ ∟ ∟ ∟ Iktyos, lamellär 1 sidobegreppX |
Bredare villkor: | |
Anmärkning: | |
Anmärkning: | A chronic, congenital ichthyosis inherited as an autosomal recessive trait. Infants are usually born encased in a collodion membrane which sheds within a few weeks. Scaling is generalized and marked with grayish-brown quadrilateral scales, adherent at their centers and free at the edges. In some cases, scales are so thick that they resemble armored plate.
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Annotation: | do not coord with INFANT, NEWBORN, DISEASES
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historyNote*: | 93; was see ICHTHYOSIFORM ERYTHRODERMA, CONGENITAL 1991-92; ERYTHRODERMA ICHTHYOSIFORME, NONBULLOUS was see ICHTHYOSIFORM ERYTHRODERMA, CONGENITAL 1991-92, was see ICHTHYOSIS 1979-90
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onlineNote*: | use ICHTHYOSIFORM ERYTHRODERMA, CONGENITAL to search ICHTHYOSIS, LAMELLAR & ERYTHRODERMA ICHTHYOSIFORME, NONBULLOUS 1991-92; use ICHTHYOSIS to search ERYTHRODERMA ICHTHYOSIFORME, NONBULLOUS 1979-90
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publicMeSHNote*: | 93; was see ICHTHYOSIFORM ERYTHRODERMA, CONGENITAL 1991-92; ERYTHRODERMA ICHTHYOSIFORME, NONBULLOUS was see ICHTHYOSIFORM ERYTHRODERMA, CONGENITAL 1991-92, was see ICHTHYOSIS 1979-90
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activeMeSHYear*: | |
dateCreated*: | 1992-05-20X |
dateEstablished*: | 1993-01-01X |
dateRevised*: | 2001-07-25X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | nnsX |
recordOriginator*: | PLSX |
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URI: | |
Termer och motsvarande begrepp: | Lamellaarinen kalansuomutauti (fi) XLamellaarinen iktyoosi (fi, ersatt) Ichthyosis, Lamellar (en) Nonbullous Congenital Ichthyosiform Erythroderma (en, ersatt) Ichthyosiform Erythroderma, Nonbullous Congenital (en, ersatt) Erythroderma Ichthyosiforme, Nonbullous (en, ersatt) Harlequin Ichthyosis (en, ersatt) Congenital Nonbullous Ichthyosiform Erythroderma (en, ersatt) Ichthyosis congenita lamellaris (la-FI, ersatt) Ichthyosis lamellaris (la-FI, ersatt) |
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