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Creutzfeldt-Jakobs syndrom
Hierarki: | ∟ ∟ ∟ ∟ Creutzfeldt-Jakobs syndrom 14 sidobegrepp∟ ∟ ∟ ∟ Creutzfeldt-Jakobs syndrom 14 sidobegrepp∟ ∟ ∟ ∟ ∟ Creutzfeldt-Jakobs syndrom 14 sidobegrepp∟ ∟ ∟ ∟ ∟ Creutzfeldt-Jakobs syndrom 14 sidobegrepp∟ ∟ ∟ ∟ Creutzfeldt-Jakobs syndrom 14 sidobegreppX |
Bredare villkor: | |
Anmärkning: | Central Nervous System Diseases (1966-1968)X |
Anmärkning: | A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes, ATAXIA; APHASIA, visual loss, weakness, muscle atrophy, MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med, 1998 Dec 31;339(27))
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historyNote*: | 91; was JAKOB-CREUTZFELDT SYNDROME 1981-90; was CREUTZFELDT-JAKOB DISEASE 1969-80 (Prov 1969-72)
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onlineNote*: | use CREUTZFELDT-JAKOB SYNDROME to search JAKOB-CREUTZFELDT SYNDROME 1981-90 & CREUTZFELDT-JAKOB DISEASE 1969-80 (as Prov 1969-72)
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publicMeSHNote*: | 91; was JAKOB-CREUTZFELDT SYNDROME 1981-90; was CREUTZFELDT-JAKOB DISEASE 1973-80
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activeMeSHYear*: | |
dateCreated*: | 1999-01-01X |
dateEstablished*: | 1973-01-01X |
dateRevised*: | 1999-11-23X |
recordAuthorizer*: | agsX |
recordMaintainer*: | agsX |
recordOriginator*: | NLMX |
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Samordna villkor: | |
URI: | |
Termer och motsvarande begrepp: | Creutzfeldt-Jakobin tauti (fi) XCreutzfeldt-Jakobin syndrooma (fi, ersatt) Creutzfeldt-Jakobin oireyhtymä (fi, ersatt) CJD (fi, ersatt) Sporadinen CJD (fi, ersatt) vCJD (sv, ersatt) Creutzfeldt-Jakob Syndrome (en) V-CJD (Variant-Creutzfeldt-Jakob Disease) (en, ersatt) Spongiform Encephalopathy, Subacute (en, ersatt) Creutzfeldt-Jakob Disease (en, ersatt) CJD Variant (V-CJD) (en, ersatt) CJD (Creutzfeldt-Jakob Disease) (en, ersatt) Creutzfeldt-Jakob Disease, New Variant (en, ersatt) Familial Creutzfeldt-Jakob Disease (en, ersatt) Jakob-Creutzfeldt Syndrome (en, ersatt) Jakob-Creutzfeldt Disease (en, ersatt) CJD (en, ersatt) Encephalopathia spongiformis subacuta (la-FI, ersatt) Syndroma Creutzfeldt-Jakob (la-FI, ersatt) Morbus Creutzfeldt-Jakob (la-FI, ersatt) |
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