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Koproporfyrinogenoxidas
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Anmärkning: | Carboxy-Lyases (1972-1974) | Coproporphyrins (1975) | Oxidoreductases (1975) | Porphyrins (1972-1974)X |
Anmärkning: | An enzyme that catalyzes the oxidative decarboxylation of coproporphyrinogen III to protoporphyrinogen IX by the conversion of two propionate groups to two vinyl groups. It is the sixth enzyme in the 8-enzyme biosynthetic pathway of HEME, and is encoded by CPO gene. Mutations of CPO gene result in HEREDITARY COPROPORPHYRIA.
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historyNote*: | 91(76); was see under OXIDOREDUCTASES 1976-90
X |
publicMeSHNote*: | 91; was see under OXIDOREDUCTASES 1976-90
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activeMeSHYear*: | |
dateCreated*: | 1975-07-25X |
dateEstablished*: | 1991-01-01X |
dateRevised*: | 2005-06-30X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | jmpX |
recordOriginator*: | RLSX |
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Termer och motsvarande begrepp: | Koproporfyrinogeenioksidaasi (fi) XCoproporphyrinogen Oxidase (en) Coproporphyrinogenase (en, ersatt) Coproporphyrinogen III Oxidases (en, ersatt) |
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