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Schilders diffusa cerebrala skleros
Hierarki: | ∟ ∟ ∟ ∟ ∟ Schilders diffusa cerebrala skleros 33 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Amblyopi | ∟ ∟ ∟ Demens | ∟ Epilepsi | ∟ ∟ Hjärndöd | ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Schilders diffusa cerebrala skleros 33 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Amblyopi | ∟ ∟ ∟ Demens | ∟ Epilepsi | ∟ ∟ Hjärndöd | ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Schilders diffusa cerebrala skleros 33 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Amblyopi | ∟ ∟ ∟ Demens | ∟ Epilepsi | ∟ ∟ Hjärndöd | ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Schilders diffusa cerebrala skleros 33 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Amblyopi | ∟ ∟ ∟ Demens | ∟ Epilepsi | ∟ ∟ Hjärndöd | ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ |
Bredare villkor: | ∟ ∟ ∟ ∟ ∟ Schilders diffusa cerebrala skleros ∟ ∟ ∟ ∟ Schilders diffusa cerebrala skleros ∟ ∟ ∟ ∟ Schilders diffusa cerebrala skleros ∟ ∟ ∟ ∟ Schilders diffusa cerebrala skleros |
Anmärkning: | A rare central nervous system demyelinating condition affecting children and young adults. Pathologic findings include a large, sharply defined, asymmetric focus of myelin destruction that may involve an entire lobe or cerebral hemisphere. The clinical course tends to be progressive and includes dementia, cortical blindness, cortical deafness, spastic hemiplegia, and pseudobulbar palsy. Concentric sclerosis of Balo is differentiated from diffuse cerebral sclerosis of Schilder by the pathologic finding of alternating bands of destruction and preservation of myelin in concentric rings. Alpers' Syndrome refers to a heterogeneous group of diseases that feature progressive cerebral deterioration and liver disease. (From Adams et al., Principles of Neurology, 6th ed, p914; Dev Neurosci 1991;13(4-5):267-73)
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historyNote*: | 2000(1963)
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publicMeSHNote*: | 2000; see CEREBRAL SCLEROSIS, DIFFUSE 1963-1999; for ENCEPHALITIS PERIAXIALIS see ENCEPHALITIS PERIAXIALIS 1963-1999; for BALO'S DISEASE, ENCEPHALITIS PERIAXIALIS DIFFUSA, MYELINOCLASTIC DIFFUSE SCLEROSIS, & SCHILDER'S DISEASE see ENCEPHALITIS PERIAXIALIS 1990-1999
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activeMeSHYear*: | |
dateCreated*: | 1999-01-01X |
dateRevised*: | 1999-11-04X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | KEVX |
recordOriginator*: | NLMX |
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Termer och motsvarande begrepp: | Schilderin tauti (fi) XSchilderin diffuusi aivokovettuma (fi, ersatt) Schilderin diffuusi aivoskleroosi (fi, ersatt) Schilderin diffuusi aivojen skleroosi (fi, ersatt) Schilderin diffuusi aivojen kovettuma (fi, ersatt) Periaksiaalinen enkefaliitti (fi, ersatt) Periaksiaalinen aivotulehdus (fi, ersatt) Periaksiaalinen aivokuume (fi, ersatt) Aivotulehdus, periaksiaalinen (fi, ersatt) Keskuskermoston diffuusi skleroosi (fi, ersatt) Encephalitis periaxialis (sv, ersatt) Schilders sjukdom (sv, ersatt) Balos koncentrisk skleros (sv, ersatt) Alpers syndrom (sv, ersatt) Diffuse Cerebral Sclerosis of Schilder (en) Encephalitis Periaxialis (en, ersatt) Encephalitis Periaxialis Concentrica (en, ersatt) Cerebral Sclerosis, Diffuse (en, ersatt) Balo's Concentric Sclerosis (en, ersatt) Alpers' Syndrome (en, ersatt) Encephalitis Periaxialis Diffusa (en, ersatt) Myelinoclastic Diffuse Sclerosis (en, ersatt) Schilder's Disease (en, ersatt) Schilder Disease (en, ersatt) Poliodystrophia Cerebri (en, ersatt) Alpers' Disease (en, ersatt) Encephalitis periaxialis (la-FI, ersatt) Morbus Schilder (la-FI, ersatt) Sclerosis diffusa (la-FI, ersatt) |
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