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Isovaleryyli-KoA-dehydrogenaasi
Hierarki: | |
Bredare villkor: | |
Anmärkning: | Acyl Coenzyme A (1980-1982) | Coenzyme A (1973-1980) | Oxidoreductases (1983-2003) | Oxidoreductases Acting on CH-CH Group Donors (2004-2005) | Valerates (1973-1982)X |
Anmärkning: | A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA).
X |
historyNote*: | 2006(1973)
X |
publicMeSHNote*: | 2006; ISOVALERYL-COA DEHYDROGENASE was indexed under OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS 2004-2005, under OXIDOREDUCTASES 1983-2003, under ACYL COENZYME A 1980-1982, COENZYME A 1973-1980, and under VALERATES 1973-1982
X |
activeMeSHYear*: | |
dateCreated*: | 2005-06-30X |
dateEstablished*: | 2006-01-01X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | AKEX |
recordOriginator*: | AKEX |
Typ: | |
Samordna villkor: | |
URI: | |
Termer och motsvarande begrepp: | Isovaleryl-CoA Dehydrogenase (en) XIsovaleryl-Coenzyme A Dehydrogenase (en, ersatt) Isovaleryl CoA Dehydrogenase (en, ersatt) |
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