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Suksinaatti-semialdehydi-dehydrogenaasi
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Anmärkning: | An enzyme that plays a role in the GLUTAMATE and butanoate metabolism pathways by catalyzing the oxidation of succinate semialdehyde to SUCCINATE using NAD+ as a coenzyme. Deficiency of this enzyme, causes 4-hydroxybutyricaciduria, a rare inborn error in the metabolism of the neurotransmitter 4-aminobutyric acid (GABA).
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historyNote*: | 2006(1980); use ALDEHYDE OXIDREDUCTASES 1977-1979
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publicMeSHNote*: | 2006; SUCCINATE-SEMIALDEHYDE DEHYDROGENASE was indexed under ALDEHYDE OXIDOREDUCTASES 1977-2005
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activeMeSHYear*: | |
dateCreated*: | 2005-06-30X |
dateEstablished*: | 2006-01-01X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | AKEX |
recordOriginator*: | AKEX |
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Termer och motsvarande begrepp: | Succinate-Semialdehyde Dehydrogenase (en) XSuccinic Semialdehyde Dehydrogenase (en, ersatt) Succinate Semialdehyde Dehydrogenase (en, ersatt) NAD(+)-Dependent Succinic Semialdehyde Dehydrogenase (en, ersatt) |
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