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Uroporfyrinogen dekarboxylas
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Anmärkning: | An enzyme that catalyzes the decarboxylation of UROPORPHYRINOGEN III to coproporphyrinogen III by the conversion of four acetate groups to four methyl groups. It is the fifth enzyme in the 8-enzyme biosynthetic pathway of HEME. Several forms of cutaneous PORPHYRIAS are results of this enzyme deficiency as in PORPHYRIA CUTANEA TARDA; and HEPATOERYTHROPOIETIC PORPHYRIA.
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Annotation: | /defic permitted but consider also PORPHYRIA CUTANEA TARDA and HEPATOERYTHROPOIETIC PORPHYRIA
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historyNote*: | 91(76); was see under CARBOXY-LYASES 1976-90
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publicMeSHNote*: | 91; was see under CARBOXY-LYASES 1976-90
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activeMeSHYear*: | |
dateCreated*: | 1975-07-25X |
dateEstablished*: | 1991-01-01X |
dateRevised*: | 2005-07-12X |
recordAuthorizer*: | agsX |
recordMaintainer*: | agsX |
recordOriginator*: | RLSX |
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Termer och motsvarande begrepp: | Uroporfyrinogeenidekarboksylaasi (fi) XUroporphyrinogen Decarboxylase (en) Uroporphyrinogen III Decarboxylase (en, ersatt) Uroporphyrinogen Carboxy-Lyase (en, ersatt) |
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