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Diamond-Blackfans anemi
Hierarki: | ∟ ∟ ∟ ∟ ∟ ∟ Diamond-Blackfans anemi 1 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ Diamond-Blackfans anemi 1 sidobegrepp∟ ∟ ∟ ∟ ∟ Diamond-Blackfans anemi 1 sidobegrepp∟ ∟ ∟ ∟ Diamond-Blackfans anemi 1 sidobegreppX |
Bredare villkor: | ∟ ∟ ∟ ∟ ∟ ∟ Diamond-Blackfans anemi ∟ ∟ ∟ ∟ ∟ ∟ Diamond-Blackfans anemi ∟ ∟ ∟ ∟ ∟ Diamond-Blackfans anemi ∟ ∟ ∟ ∟ Diamond-Blackfans anemi |
Anmärkning: | |
Anmärkning: | A rare congenital hypoplastic anemia that usually presents early in infancy. The disease is characterized by a moderate to severe macrocytic anemia, occasional neutropenia or thrombocytosis, a normocellular bone marrow with erythroid hypoplasia, and an increased risk of developing leukemia. (Curr Opin Hematol 2000 Mar;7(2):85-94)
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historyNote*: | 2002; use FANCONI ANEMIA 1992-2001
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publicMeSHNote*: | 2002; see FANCONI ANEMIA 1992-2001
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activeMeSHYear*: | |
dateCreated*: | 2001-07-25X |
dateEstablished*: | 2002-01-01X |
Typ: | |
Samordna villkor: | |
URI: | |
Termer och motsvarande begrepp: | Diamond-Blackfanin anemia (fi) XDiamond-Blackfanin oireyhtymä (fi, ersatt) Diamond-Blackfanin syndrooma (fi, ersatt) Blackfan-Diamondin syndrooma (fi, ersatt) Blackfan-Diamondin oireyhtymä (fi, ersatt) Blackfan-Diamondin anemia (fi, ersatt) Anemia, Diamond-Blackfan (en) Diamond-Blackfan Anemia (en, ersatt) |
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