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Landau-Kleffners syndrom
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Anmärkning: | A syndrome characterized by the onset of isolated language dysfunction in otherwise normal children (age of onset 4-7 years) and epileptiform discharges on ELECTROENCEPHALOGRAPHY. Seizures, including atypical absence (EPILEPSY, ABSENCE), complex partial (EPILEPSY, COMPLEX PARTIAL), and other types may occur. The electroencephalographic abnormalities and seizures tend to resolve by puberty. The language disorder may also resolve although some individuals are left with severe language dysfunction, including APHASIA and auditory AGNOSIA. (From Menkes, Textbook of Child Neurology, 5th ed, pp749-50; J Child Neurol 1997 Nov;12(8):489-495)
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historyNote*: | 1996
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publicMeSHNote*: | 1996
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activeMeSHYear*: | |
dateCreated*: | 1994-12-27X |
dateEstablished*: | 1996-01-01X |
dateRevised*: | 2001-07-25X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | agsX |
recordOriginator*: | TGCX |
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Termer och motsvarande begrepp: | Landau-Kleffnerin oireyhtymä (fi) XLandau-Kleffnerin syndrooma (fi, ersatt) Epileptinen afasia (fi, ersatt) Landau-Kleffner Syndrome (en) Landau-Kleffner Acquired Epileptiform Aphasia (en, ersatt) Aphasia, Acquired Epileptic (en, ersatt) Aphasia, Epileptic, Acquired (en, ersatt) Acquired Childhoood Aphasia with Convulsive Disorder (en, ersatt) Aphasia acquisita epileptica (la-FI, ersatt) Syndroma Landau-Kleffner (la-FI, ersatt) |
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