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Subakut skleroserande panencefalit
Hierarki: | ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit 13 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit 13 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit 13 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit 13 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit 13 sidobegrepp∟ ∟ ∟ Subakut skleroserande panencefalit 13 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit 13 sidobegrepp∟ ∟ ∟ Subakut skleroserande panencefalit 13 sidobegrepp∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit 13 sidobegreppX |
Bredare villkor: | ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit ∟ ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit ∟ ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit ∟ ∟ ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit ∟ ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit ∟ ∟ ∟ Subakut skleroserande panencefalit ∟ ∟ ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit ∟ ∟ ∟ Subakut skleroserande panencefalit ∟ ∟ ∟ ∟ ∟ Subakut skleroserande panencefalit |
Anmärkning: | Cerebral Sclerosis, Diffuse (1966-1970)X |
Anmärkning: | A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8)
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historyNote*: | 71; VAN BOGAERT'S LEUKOENCEPHALITIS was see under SUBACUTE SCLEROSING PANENCEPHALITIS 1971-78; was see under CEREBRAL SCLEROSIS, DIFFUSE 1963-70
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onlineNote*: | use SUBACUTE SCLEROSING PANENCEPHALITIS to search VAN BOGAERT'S LEUKOENCEPHALITIS 1971-78; use CEREBRAL SCLEROSIS, DIFFUSE 1966-70
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publicMeSHNote*: | 71; VAN BOGAERT'S LEUKOENCEPHALITIS was see under SUBACUTE SCLEROSING PANENCEPHALITIS 1971-78; was see under CEREBRAL SCLEROSIS, DIFFUSE 1963-70
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activeMeSHYear*: | |
dateCreated*: | 1999-01-01X |
dateEstablished*: | 1971-01-01X |
dateRevised*: | 2001-08-03X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | sjnX |
recordOriginator*: | NLMX |
Typ: | |
Samordna villkor: | |
URI: | |
Termer och motsvarande begrepp: | Subakuutti sklerosoiva panenkefaliitti (fi) XVan Bogaertin sklerosoiva leukoenkefalopatia (fi, ersatt) SSPE (fi, ersatt) Panenkefaliitti, subakuutti sklerosoiva (fi, ersatt) Dawsonin inkluusiokappale -aivotulehdus (fi, ersatt) SSPE (sv, ersatt) Subacute Sclerosing Panencephalitis (en) Van Bogaert's Leukoencephalitis (en, ersatt) Leukoencephalitis, Van Bogaert's (en, ersatt) Leukoencephalitis, Subacute Sclerosing (en, ersatt) Inclusion Body Encephalitis, Measles (en, ersatt) Measles Inclusion Body Encephalitis (en, ersatt) Panencephalitis, Subacute Sclerosing (en, ersatt) SSPE (en, ersatt) Sclerosing Panencephalitis, Subacute (en, ersatt) Sclerosing Leukoencephalitis, Subacute (en, ersatt) Encephaltis, Inclusion Body, Measles (en, ersatt) Encephalitis cum corporibus inclusionis Dawson (la-FI, ersatt) Leucoencephalopathia sclerosificans Van Bogaert (la-FI, ersatt) Panencephalitis sclerosificans subacuta (la-FI, ersatt) Panencephalitis sclerosans subacuta (la-FI, ersatt) |
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