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Muskelatrofi, spinal
Hierarki: | ∟ ∟ ∟ ∟ Muskelatrofi, spinal 21 sidobegrepp1 underordnad begrepp∟ ∟ ∟ ∟ Muskelatrofi, spinal 21 sidobegrepp1 underordnad begrepp∟ ∟ ∟ ∟ Muskelatrofi, spinal 21 sidobegrepp1 underordnad begrepp∟ ∟ ∟ Muskelatrofi, spinal 21 sidobegrepp1 underordnad begreppX |
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Anmärkning: | A group of disorders marked by progressive degeneration of motor neurons in the spinal cord resulting in weakness and muscular atrophy, usually without evidence of injury to the corticospinal tracts. Diseases in this category include Werdnig-Hoffmann disease and later onset SPINAL MUSCULAR ATROPHIES OF CHILDHOOD, most of which are hereditary. (Adams et al., Principles of Neurology, 6th ed, p1089)
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Annotation: | MUSCULAR ATROPHY, SPINAL, INFANTILE see SPINAL MUSCULAR ATROPHIES OF CHILDHOOD is also available
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historyNote*: | 1988
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publicMeSHNote*: | 1988
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activeMeSHYear*: | |
dateCreated*: | 1987-03-10X |
dateEstablished*: | 1988-01-01X |
dateRevised*: | 2001-07-25X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | agsX |
recordOriginator*: | SDX |
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Termer och motsvarande begrepp: | Spinaalinen lihasatrofia (fi) XHermoperäinen lihassurkastuma (fi, ersatt) Spinaalinen lihassurkastuma (fi, ersatt) Spinaalinen lihasten surkastuminen (fi, ersatt) Spinal muskelatrofi (sv, ersatt) Muscular Atrophy, Spinal (en) X-Linked Bulbo-Spinal Atrophy (en, ersatt) Spinal Muscular Atrophy, Scapuloperoneal Form (en, ersatt) Spinal Muscular Atrophy, Oculopharyngeal (en, ersatt) Spinal Muscular Atrophy, Distal (en, ersatt) Kennedy Syndrome (en, ersatt) Bulbo-Spinal Atrophy, X-Linked (en, ersatt) Myelopathic Muscular Atrophy, Progressive (en, ersatt) Progressive Myelopathic Muscular Atrophy (en, ersatt) Spinal Muscular Atrophy (en, ersatt) Proximal Myelopathic Muscular Atrophy, Progressive (en, ersatt) Adult Spinal Muscular Atrophy (en, ersatt) |
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