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Hemoglobinuri, paroxysmal
Hierarki: | ∟ ∟ ∟ ∟ ∟ Hemoglobinuri, paroxysmal 8 sidobegrepp∟ ∟ ∟ ∟ ∟ Hemoglobinuri, paroxysmal 8 sidobegreppX |
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Anmärkning: | A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins.
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historyNote*: | 78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77
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onlineNote*: | use HEMOGLOBINURIA, PAROXYSMAL to search MARCHIAFAVA-MICHELI SYNDROME 1966-77
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publicMeSHNote*: | 78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77
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activeMeSHYear*: | 2007X |
dateCreated*: | 1999-01-01X |
dateRevised*: | 2006-07-05X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | lktX |
recordOriginator*: | NLMX |
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Termer och motsvarande begrepp: | Paroksysmaalinen hemoglobinuria (fi) XMarchiafavan tauti (fi, ersatt) Marchiafava-Michelin tauti (fi, ersatt) Paroksysmaalinen nokturnaalinen hemoglobinuria (fi, ersatt) PNH (fi, ersatt) Kohtauksittainen yöllinen verenpunavirtsaisuus (fi, ersatt) Kohtauksittainen yöllinen hemoglobiinivirtsaisuus (fi, ersatt) Hemoglobinuria, paroksysmaalinen (fi, ersatt) Kohtauksittainen verenpunavirtsaisuus (fi, ersatt) Kohtauksittainen hemoglobiinivirtsaisuus (fi, ersatt) Hemoglobinuria, Paroxysmal (en) Paroxysmal Hemoglobinuria, Cold (en, ersatt) Paroxysmal Hemoglobinuria (en, ersatt) Paroxysmal Hemoglobinuria, Nocturnal (en, ersatt) Marchiafava-Micheli Syndrome (en, ersatt) Haemoglobinuria paroxysmalis nocturna (la-FI, ersatt) Haemoglobinuria nocturna (la-FI, ersatt) |
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