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Enzymsystem för glykogennedbrytning
Hierarki: | ∟ ∟ ∟ ∟ ∟ ∟ Enzymsystem för glykogennedbrytning 9 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Enzymsystem för glykogennedbrytning 9 sidobegrepp∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ |
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Anmärkning: | 1,4-alpha-D-Glucan-1,4-alpha-D-glucan 4-alpha-D-glucosyltransferase/dextrin 6 alpha-D-glucanohydrolase. An enzyme system having both 4-alpha-glucanotransferase (EC 2.4.1.25) and amylo-1,6-glucosidase (EC 3.2.1.33) activities. As a transferase it transfers a segment of a 1,4-alpha-D-glucan to a new 4-position in an acceptor, which may be glucose or another 1,4-alpha-D-glucan. As a glucosidase it catalyzes the endohydrolysis of 1,6-alpha-D-glucoside linkages at points of branching in chains of 1,4-linked alpha-D-glucose residues. Amylo-1,6-glucosidase activity is deficient in glycogen storage disease type III.
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Annotation: | /defic: consider also GLYCOGEN STORAGE DISEASE TYPE III
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historyNote*: | 89(76); was GLYCOGEN DEBRANCHING ENZYME see under GLUCOSYLTRANSFERASES 1976-88
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onlineNote*: | use GLYCOGEN DEBRANCHING ENZYME SYSTEM to search GLYCOGEN DEBRANCHING ENZYME 1976-88
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publicMeSHNote*: | 89; was GLYCOGEN DEBRANCHING ENZYME see under GLUCOSYLTRANSFERASES 1976-88
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activeMeSHYear*: | |
dateCreated*: | 1975-07-21X |
dateEstablished*: | 1989-01-01X |
dateRevised*: | 2003-07-09X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | ssbX |
recordOriginator*: | RLSX |
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Termer och motsvarande begrepp: | Glykogeenia pilkkova entsyymijärjestelmä (fi) XGlycogen Debranching Enzyme System (en) Transfer-Glucosidase (en, ersatt) |
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