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Paralysis, Hyperkalemic Periodic
Hierarchy: | ∟ ∟ ∟ ∟ ∟ ∟ Paralysis, Hyperkalemic Periodic 1 coordinate concept∟ ∟ ∟ ∟ Paralysis, Hyperkalemic Periodic 1 coordinate concept∟ ∟ ∟ ∟ ∟ Paralysis, Hyperkalemic Periodic 1 coordinate concept∟ ∟ ∟ ∟ ∟ ∟ Paralysis, Hyperkalemic Periodic 1 coordinate conceptX |
Broader terms: | ∟ ∟ ∟ ∟ ∟ ∟ Paralysis, Hyperkalemic Periodic ∟ ∟ ∟ ∟ Paralysis, Hyperkalemic Periodic ∟ ∟ ∟ ∟ ∟ Paralysis, Hyperkalemic Periodic ∟ ∟ ∟ ∟ ∟ ∟ Paralysis, Hyperkalemic Periodic |
History note: | Paralyses, Familial Periodic (1966-1999)X |
historyNote*: | 2000
X |
publicMeSHNote*: | 2000
X |
Scope note: | An autosomal dominant familial disorder which presents in infancy or childhood and is characterized by episodes of weakness associated with hyperkalemia. During attacks, muscles of the lower extremities are initially affected, followed by the lower trunk and arms. Episodes last from 15-60 minutes and typically occur after a period of rest following exercise. A defect in skeletal muscle sodium channels has been identified as the cause of this condition. Normokalemic periodic paralysis is a closely related disorder marked by a lack of alterations in potassium levels during attacks of weakness. (Adams et al., Principles of Neurology, 6th ed, p1481)
X |
activeMeSHYear*: | 2007X |
dateCreated*: | 1999-11-03X |
dateEstablished*: | 2000-01-01X |
dateRevised*: | 2006-07-05X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | lktX |
recordOriginator*: | KEVX |
Related term: | |
Type: | |
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Labels and equivalent concepts: | Hyperkaleeminen periodinen halvaus (fi) XMyotoninen jaksoittainen paralyysi (fi, replaced) Myotoninen periodinen paralyysi (fi, replaced) Myotoninen jaksoittainen halvaus (fi, replaced) Hyperkaleminen periodinen paralyysi (fi, replaced) Hyperkaleminen jaksoittainen halvaus (fi, replaced) Hyperkaleminen jaksoittainen paralyysi (fi, replaced) Suvuittainen hyperkaleeminen periodinen paralyysi (fi, replaced) Suvuittainen jaksoittainen halvaus (fi, replaced) Suvuittainen myotoninen periodinen paralyysi (fi, replaced) Suvuittainen myotoninen jaksoittainen paralyysi (fi, replaced) Suvuittainen jaksoittainen paralyysi (fi, replaced) Suvuittainen myotoninen jaksoittainen halvaus (fi, replaced) Hyperkaleeminen periodinen paralyysi (fi, replaced) Hyperkaleeminen jaksoittainen paralyysi (fi, replaced) Familiaalinen hyperkaleeminen periodinen paralyysi (fi, replaced) Familiaalinen jaksoittainen halvaus (fi, replaced) Familiaalinen myotoninen periodinen paralyysi (fi, replaced) Hyperkaleeminen jaksoittainen halvaus (fi, replaced) Familiaalinen myotoninen jaksoittainen paralyysi (fi, replaced) Familiaalinen myotoninen jaksoittainen halvaus (fi, replaced) Familiaalinen jaksoittainen paralyysi (fi, replaced) Paralys, hyperkalemisk periodisk (sv) Hyperkalemisk periodisk paralys (sv, replaced) Myotonisk periodisk paralys (sv, replaced) Paralysis, Periodic, Hyperkalemic, Familial (en, replaced) Primary Hyperkalemic Periodic Paralysis (en, replaced) Myotonic Periodic Paralysis (en, replaced) Hyperkalemic Periodic Paralysis, Familial (en, replaced) Familial Hyperkalemic Periodic Paralysis (en, replaced) Hyperkalemic Periodic Paralysis (en, replaced) Adynamia Episodica Hereditaria (en, replaced) |
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