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Wiskott-Aldrich Syndrome

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Hierarchy:	Medical Subject Headings (MeSH) ∟ Congenital, Hereditary, and Neonatal Diseases and Abnormalities ∟ Genetic Diseases, Inborn ∟ Blood Coagulation Disorders, Inherited ∟ Wiskott-Aldrich Syndrome 54 coordinate concepts ∟ Afibrinogenemia \| ∟ Bernard-Soulier Syndrome \| ∟ Disseminated Intravascular Coagulation \| ∟ Factor V Deficiency \| ∟ Factor VII Deficiency \| ∟ Factor X Deficiency \| ∟ Factor XI Deficiency \| ∟ Factor XII Deficiency \| ∟ Factor XIII Deficiency \| ∟ Hemophilia A \| ∟ Hemophilia B \| ∟ Hypoprothrombinemias \| ∟ Platelet Storage Pool Deficiency \| ∟ Purpura, Thrombocytopenic, Idiopathic \| ∟ Thrombasthenia \| ∟ Thrombocythemia, Hemorrhagic \| ∟ Vascular Hemostatic Disorders \| ∟ Vitamin K Deficiency \| ∟ von Willebrand Disease \| ∟ Waterhouse-Friderichsen Syndrome \| ∟ Androgen-Insensitivity Syndrome \| ∟ Choroideremia \| ∟ Dyskeratosis Congenita \| ∟ Ectodermal Dysplasia 1, Anhidrotic \| ∟ Fabry Disease \| ∟ Focal Dermal Hypoplasia \| ∟ Glycogen Storage Disease Type IIb \| ∟ Glycogen Storage Disease Type VIII \| ∟ Granulomatous Disease, Chronic \| ∟ Hyper-IgM Immunodeficiency Syndrome, Type 1 \| ∟ Hypophosphatemic Rickets, X-Linked Dominant \| ∟ Ichthyosis, X-Linked \| ∟ Mental Retardation, X-Linked \| ∟ Muscular Dystrophy, Duchenne \| ∟ Muscular Dystrophy, Emery-Dreifuss \| ∟ Oculocerebrorenal Syndrome \| ∟ Pelizaeus-Merzbacher Disease \| ∟ X-Linked Combined Immunodeficiency Diseases \| ∟ Activated Protein C Resistance \| ∟ Antithrombin III Deficiency \| ∟ Hermanski-Pudlak Syndrome \| ∟ Protein C Deficiency \| ∟ Purpura, Thrombotic Thrombocytopenic \| ∟ Agammaglobulinemia \| ∟ Ataxia Telangiectasia \| ∟ Common Variable Immunodeficiency \| ∟ Deltaretrovirus Infections \| ∟ DiGeorge Syndrome \| ∟ Dysgammaglobulinemia \| ∟ HIV Infections \| ∟ Leukocyte-Adhesion Deficiency Syndrome \| ∟ Lymphopenia \| ∟ Phagocyte Bactericidal Dysfunction \| ∟ Severe Combined Immunodeficiency Medical Subject Headings (MeSH) ∟ Congenital, Hereditary, and Neonatal Diseases and Abnormalities ∟ Genetic Diseases, Inborn ∟ Genetic Diseases, X-Linked ∟ Wiskott-Aldrich Syndrome 54 coordinate concepts ∟ Afibrinogenemia \| ∟ Bernard-Soulier Syndrome \| ∟ Disseminated Intravascular Coagulation \| ∟ Factor V Deficiency \| ∟ Factor VII Deficiency \| ∟ Factor X Deficiency \| ∟ Factor XI Deficiency \| ∟ Factor XII Deficiency \| ∟ Factor XIII Deficiency \| ∟ Hemophilia A \| ∟ Hemophilia B \| ∟ Hypoprothrombinemias \| ∟ Platelet Storage Pool Deficiency \| ∟ Purpura, Thrombocytopenic, Idiopathic \| ∟ Thrombasthenia \| ∟ Thrombocythemia, Hemorrhagic \| ∟ Vascular Hemostatic Disorders \| ∟ Vitamin K Deficiency \| ∟ von Willebrand Disease \| ∟ Waterhouse-Friderichsen Syndrome \| ∟ Androgen-Insensitivity Syndrome \| ∟ Choroideremia \| ∟ Dyskeratosis Congenita \| ∟ Ectodermal Dysplasia 1, Anhidrotic \| ∟ Fabry Disease \| ∟ Focal Dermal Hypoplasia \| ∟ Glycogen Storage Disease Type IIb \| ∟ Glycogen Storage Disease Type VIII \| ∟ Granulomatous Disease, Chronic \| ∟ Hyper-IgM Immunodeficiency Syndrome, Type 1 \| ∟ Hypophosphatemic Rickets, X-Linked Dominant \| ∟ Ichthyosis, X-Linked \| ∟ Mental Retardation, X-Linked \| ∟ Muscular Dystrophy, Duchenne \| ∟ Muscular Dystrophy, Emery-Dreifuss \| ∟ Oculocerebrorenal Syndrome \| ∟ Pelizaeus-Merzbacher Disease \| ∟ X-Linked Combined Immunodeficiency Diseases \| ∟ Activated Protein C Resistance \| ∟ Antithrombin III Deficiency \| ∟ Hermanski-Pudlak Syndrome \| ∟ Protein C Deficiency \| ∟ Purpura, Thrombotic Thrombocytopenic \| ∟ Agammaglobulinemia \| ∟ Ataxia Telangiectasia \| ∟ Common Variable Immunodeficiency \| ∟ Deltaretrovirus Infections \| ∟ DiGeorge Syndrome \| ∟ Dysgammaglobulinemia \| ∟ HIV Infections \| ∟ Leukocyte-Adhesion Deficiency Syndrome \| ∟ Lymphopenia \| ∟ Phagocyte Bactericidal Dysfunction \| ∟ Severe Combined Immunodeficiency Medical Subject Headings (MeSH) ∟ Hemic and Lymphatic Diseases ∟ Hematologic Diseases ∟ Blood Coagulation Disorders ∟ Blood Coagulation Disorders, Inherited ∟ Wiskott-Aldrich Syndrome 54 coordinate concepts ∟ Afibrinogenemia \| ∟ Bernard-Soulier Syndrome \| ∟ Disseminated Intravascular Coagulation \| ∟ Factor V Deficiency \| ∟ Factor VII Deficiency \| ∟ Factor X Deficiency \| ∟ Factor XI Deficiency \| ∟ Factor XII Deficiency \| ∟ Factor XIII Deficiency \| ∟ Hemophilia A \| ∟ Hemophilia B \| ∟ Hypoprothrombinemias \| ∟ Platelet Storage Pool Deficiency \| ∟ Purpura, Thrombocytopenic, Idiopathic \| ∟ Thrombasthenia \| ∟ Thrombocythemia, Hemorrhagic \| ∟ Vascular Hemostatic Disorders \| ∟ Vitamin K Deficiency \| ∟ von Willebrand Disease \| ∟ Waterhouse-Friderichsen Syndrome \| ∟ Androgen-Insensitivity Syndrome \| ∟ Choroideremia \| ∟ Dyskeratosis Congenita \| ∟ Ectodermal Dysplasia 1, Anhidrotic \| ∟ Fabry Disease \| ∟ Focal Dermal Hypoplasia \| ∟ Glycogen Storage Disease Type IIb \| ∟ Glycogen Storage Disease Type VIII \| ∟ Granulomatous Disease, Chronic \| ∟ Hyper-IgM Immunodeficiency Syndrome, Type 1 \| ∟ Hypophosphatemic Rickets, X-Linked Dominant \| ∟ Ichthyosis, X-Linked \| ∟ Mental Retardation, X-Linked \| ∟ Muscular Dystrophy, Duchenne \| ∟ Muscular Dystrophy, Emery-Dreifuss \| ∟ Oculocerebrorenal Syndrome \| ∟ Pelizaeus-Merzbacher Disease \| ∟ X-Linked Combined Immunodeficiency Diseases \| ∟ Activated Protein C Resistance \| ∟ Antithrombin III Deficiency \| ∟ Hermanski-Pudlak Syndrome \| ∟ Protein C Deficiency \| ∟ Purpura, Thrombotic Thrombocytopenic \| ∟ Agammaglobulinemia \| ∟ Ataxia Telangiectasia \| ∟ Common Variable Immunodeficiency \| ∟ Deltaretrovirus Infections \| ∟ DiGeorge Syndrome \| ∟ Dysgammaglobulinemia \| ∟ HIV Infections \| ∟ Leukocyte-Adhesion Deficiency Syndrome \| ∟ Lymphopenia \| ∟ Phagocyte Bactericidal Dysfunction \| ∟ Severe Combined Immunodeficiency Medical Subject Headings (MeSH) ∟ Hemic and Lymphatic Diseases ∟ Hematologic Diseases ∟ Blood Coagulation Disorders ∟ Purpura ∟ Purpura, Thrombocytopenic ∟ Wiskott-Aldrich Syndrome 54 coordinate concepts ∟ Afibrinogenemia \| ∟ Bernard-Soulier Syndrome \| ∟ Disseminated Intravascular Coagulation \| ∟ Factor V Deficiency \| ∟ Factor VII Deficiency \| ∟ Factor X Deficiency \| ∟ Factor XI Deficiency \| ∟ Factor XII Deficiency \| ∟ Factor XIII Deficiency \| ∟ Hemophilia A \| ∟ Hemophilia B \| ∟ Hypoprothrombinemias \| ∟ Platelet Storage Pool Deficiency \| ∟ Purpura, Thrombocytopenic, Idiopathic \| ∟ Thrombasthenia \| ∟ Thrombocythemia, Hemorrhagic \| ∟ Vascular Hemostatic Disorders \| ∟ Vitamin K Deficiency \| ∟ von Willebrand Disease \| ∟ Waterhouse-Friderichsen Syndrome \| ∟ Androgen-Insensitivity Syndrome \| ∟ Choroideremia \| ∟ Dyskeratosis Congenita \| ∟ Ectodermal Dysplasia 1, Anhidrotic \| ∟ Fabry Disease \| ∟ Focal Dermal Hypoplasia \| ∟ Glycogen Storage Disease Type IIb \| ∟ Glycogen Storage Disease Type VIII \| ∟ Granulomatous Disease, Chronic \| ∟ Hyper-IgM Immunodeficiency Syndrome, Type 1 \| ∟ Hypophosphatemic Rickets, X-Linked Dominant \| ∟ Ichthyosis, X-Linked \| ∟ Mental Retardation, X-Linked \| ∟ Muscular Dystrophy, Duchenne \| ∟ Muscular Dystrophy, Emery-Dreifuss \| ∟ Oculocerebrorenal Syndrome \| ∟ Pelizaeus-Merzbacher Disease \| ∟ X-Linked Combined Immunodeficiency Diseases \| ∟ Activated Protein C Resistance \| ∟ Antithrombin III Deficiency \| ∟ Hermanski-Pudlak Syndrome \| ∟ Protein C Deficiency \| ∟ Purpura, Thrombotic Thrombocytopenic \| ∟ Agammaglobulinemia \| ∟ Ataxia Telangiectasia \| ∟ Common Variable Immunodeficiency \| ∟ Deltaretrovirus Infections \| ∟ DiGeorge Syndrome \| ∟ Dysgammaglobulinemia \| ∟ HIV Infections \| ∟ Leukocyte-Adhesion Deficiency Syndrome \| ∟ Lymphopenia \| ∟ Phagocyte Bactericidal Dysfunction \| ∟ Severe Combined Immunodeficiency Medical Subject Headings (MeSH) ∟ Hemic and Lymphatic Diseases ∟ Hematologic Diseases ∟ Blood Coagulation Disorders ∟ Purpura, Thrombocytopenic ∟ Wiskott-Aldrich Syndrome 54 coordinate concepts ∟ Afibrinogenemia \| ∟ Bernard-Soulier Syndrome \| ∟ Disseminated Intravascular Coagulation \| ∟ Factor V Deficiency \| ∟ Factor VII Deficiency \| ∟ Factor X Deficiency \| ∟ Factor XI Deficiency \| ∟ Factor XII Deficiency \| ∟ Factor XIII Deficiency \| ∟ Hemophilia A \| ∟ Hemophilia B \| ∟ Hypoprothrombinemias \| ∟ Platelet Storage Pool Deficiency \| ∟ Purpura, Thrombocytopenic, Idiopathic \| ∟ Thrombasthenia \| ∟ Thrombocythemia, Hemorrhagic \| ∟ Vascular Hemostatic Disorders \| ∟ Vitamin K Deficiency \| ∟ von Willebrand Disease \| ∟ Waterhouse-Friderichsen Syndrome \| ∟ Androgen-Insensitivity Syndrome \| ∟ Choroideremia \| ∟ Dyskeratosis Congenita \| ∟ Ectodermal Dysplasia 1, Anhidrotic \| ∟ Fabry Disease \| ∟ Focal Dermal Hypoplasia \| ∟ Glycogen Storage Disease Type IIb \| ∟ Glycogen Storage Disease Type VIII \| ∟ Granulomatous Disease, Chronic \| ∟ Hyper-IgM Immunodeficiency Syndrome, Type 1 \| ∟ Hypophosphatemic Rickets, X-Linked Dominant \| ∟ Ichthyosis, X-Linked \| ∟ Mental Retardation, X-Linked \| ∟ Muscular Dystrophy, Duchenne \| ∟ Muscular Dystrophy, Emery-Dreifuss \| ∟ Oculocerebrorenal Syndrome \| ∟ Pelizaeus-Merzbacher Disease \| ∟ X-Linked Combined Immunodeficiency Diseases \| ∟ Activated Protein C Resistance \| ∟ Antithrombin III Deficiency \| ∟ Hermanski-Pudlak Syndrome \| ∟ Protein C Deficiency \| ∟ Purpura, Thrombotic Thrombocytopenic \| ∟ Agammaglobulinemia \| ∟ Ataxia Telangiectasia \| ∟ Common Variable Immunodeficiency \| ∟ Deltaretrovirus Infections \| ∟ DiGeorge Syndrome \| ∟ Dysgammaglobulinemia \| ∟ HIV Infections \| ∟ Leukocyte-Adhesion Deficiency Syndrome \| ∟ Lymphopenia \| ∟ Phagocyte Bactericidal Dysfunction \| ∟ Severe Combined Immunodeficiency Medical Subject Headings (MeSH) ∟ Hemic and Lymphatic Diseases ∟ Hematologic Diseases ∟ Blood Platelet Disorders ∟ Thrombocytopenia ∟ Purpura, Thrombocytopenic ∟ Wiskott-Aldrich Syndrome 54 coordinate concepts ∟ Afibrinogenemia \| ∟ Bernard-Soulier Syndrome \| ∟ Disseminated Intravascular Coagulation \| ∟ Factor V Deficiency \| ∟ Factor VII Deficiency \| ∟ Factor X Deficiency \| ∟ Factor XI Deficiency \| ∟ Factor XII Deficiency \| ∟ Factor XIII Deficiency \| ∟ Hemophilia A \| ∟ Hemophilia B \| ∟ Hypoprothrombinemias \| ∟ Platelet Storage Pool Deficiency \| ∟ Purpura, Thrombocytopenic, Idiopathic \| ∟ Thrombasthenia \| ∟ Thrombocythemia, Hemorrhagic \| ∟ Vascular Hemostatic Disorders \| ∟ Vitamin K Deficiency \| ∟ von Willebrand Disease \| ∟ Waterhouse-Friderichsen Syndrome \| ∟ Androgen-Insensitivity Syndrome \| ∟ Choroideremia \| ∟ Dyskeratosis Congenita \| ∟ Ectodermal Dysplasia 1, Anhidrotic \| ∟ Fabry Disease \| ∟ Focal Dermal Hypoplasia \| ∟ Glycogen Storage Disease Type IIb \| ∟ Glycogen Storage Disease Type VIII \| ∟ Granulomatous Disease, Chronic \| ∟ Hyper-IgM Immunodeficiency Syndrome, Type 1 \| ∟ Hypophosphatemic Rickets, X-Linked Dominant \| ∟ Ichthyosis, X-Linked \| ∟ Mental Retardation, X-Linked \| ∟ Muscular Dystrophy, Duchenne \| ∟ Muscular Dystrophy, Emery-Dreifuss \| ∟ Oculocerebrorenal Syndrome \| ∟ Pelizaeus-Merzbacher Disease \| ∟ X-Linked Combined Immunodeficiency Diseases \| ∟ Activated Protein C Resistance \| ∟ Antithrombin III Deficiency \| ∟ Hermanski-Pudlak Syndrome \| ∟ Protein C Deficiency \| ∟ Purpura, Thrombotic Thrombocytopenic \| ∟ Agammaglobulinemia \| ∟ Ataxia Telangiectasia \| ∟ Common Variable Immunodeficiency \| ∟ Deltaretrovirus Infections \| ∟ DiGeorge Syndrome \| ∟ Dysgammaglobulinemia \| ∟ HIV Infections \| ∟ Leukocyte-Adhesion Deficiency Syndrome \| ∟ Lymphopenia \| ∟ Phagocyte Bactericidal Dysfunction \| ∟ Severe Combined Immunodeficiency Medical Subject Headings (MeSH) ∟ Hemic and Lymphatic Diseases ∟ Hematologic Diseases ∟ Hemorrhagic Disorders ∟ Wiskott-Aldrich Syndrome 54 coordinate concepts ∟ Afibrinogenemia \| ∟ Bernard-Soulier Syndrome \| ∟ Disseminated Intravascular Coagulation \| ∟ Factor V Deficiency \| ∟ Factor VII Deficiency \| ∟ Factor X Deficiency \| ∟ Factor XI Deficiency \| ∟ Factor XII Deficiency \| ∟ Factor XIII Deficiency \| ∟ Hemophilia A \| ∟ Hemophilia B \| ∟ Hypoprothrombinemias \| ∟ Platelet Storage Pool Deficiency \| ∟ Purpura, Thrombocytopenic, Idiopathic \| ∟ Thrombasthenia \| ∟ Thrombocythemia, Hemorrhagic \| ∟ Vascular Hemostatic Disorders \| ∟ Vitamin K Deficiency \| ∟ von Willebrand Disease \| ∟ Waterhouse-Friderichsen Syndrome \| ∟ Androgen-Insensitivity Syndrome \| ∟ Choroideremia \| ∟ Dyskeratosis Congenita \| ∟ Ectodermal Dysplasia 1, Anhidrotic \| ∟ Fabry Disease \| ∟ Focal Dermal Hypoplasia \| ∟ Glycogen Storage Disease Type IIb \| ∟ Glycogen Storage Disease Type VIII \| ∟ Granulomatous Disease, Chronic \| ∟ Hyper-IgM Immunodeficiency Syndrome, Type 1 \| ∟ Hypophosphatemic Rickets, X-Linked Dominant \| ∟ Ichthyosis, X-Linked \| ∟ Mental Retardation, X-Linked \| ∟ Muscular Dystrophy, Duchenne \| ∟ Muscular Dystrophy, Emery-Dreifuss \| ∟ Oculocerebrorenal Syndrome \| ∟ Pelizaeus-Merzbacher Disease \| ∟ X-Linked Combined Immunodeficiency Diseases \| ∟ Activated Protein C Resistance \| ∟ Antithrombin III Deficiency \| ∟ Hermanski-Pudlak Syndrome \| ∟ Protein C Deficiency \| ∟ Purpura, Thrombotic Thrombocytopenic \| ∟ Agammaglobulinemia \| ∟ Ataxia Telangiectasia \| ∟ Common Variable Immunodeficiency \| ∟ Deltaretrovirus Infections \| ∟ DiGeorge Syndrome \| ∟ Dysgammaglobulinemia \| ∟ HIV Infections \| ∟ Leukocyte-Adhesion Deficiency Syndrome \| ∟ Lymphopenia \| ∟ Phagocyte Bactericidal Dysfunction \| ∟ Severe Combined Immunodeficiency Medical Subject Headings (MeSH) ∟ Immune System Diseases ∟ Immunologic Deficiency Syndromes ∟ Wiskott-Aldrich Syndrome 54 coordinate concepts ∟ Afibrinogenemia \| ∟ Bernard-Soulier Syndrome \| ∟ Disseminated Intravascular Coagulation \| ∟ Factor V Deficiency \| ∟ Factor VII Deficiency \| ∟ Factor X Deficiency \| ∟ Factor XI Deficiency \| ∟ Factor XII Deficiency \| ∟ Factor XIII Deficiency \| ∟ Hemophilia A \| ∟ Hemophilia B \| ∟ Hypoprothrombinemias \| ∟ Platelet Storage Pool Deficiency \| ∟ Purpura, Thrombocytopenic, Idiopathic \| ∟ Thrombasthenia \| ∟ Thrombocythemia, Hemorrhagic \| ∟ Vascular Hemostatic Disorders \| ∟ Vitamin K Deficiency \| ∟ von Willebrand Disease \| ∟ Waterhouse-Friderichsen Syndrome \| ∟ Androgen-Insensitivity Syndrome \| ∟ Choroideremia \| ∟ Dyskeratosis Congenita \| ∟ Ectodermal Dysplasia 1, Anhidrotic \| ∟ Fabry Disease \| ∟ Focal Dermal Hypoplasia \| ∟ Glycogen Storage Disease Type IIb \| ∟ Glycogen Storage Disease Type VIII \| ∟ Granulomatous Disease, Chronic \| ∟ Hyper-IgM Immunodeficiency Syndrome, Type 1 \| ∟ Hypophosphatemic Rickets, X-Linked Dominant \| ∟ Ichthyosis, X-Linked \| ∟ Mental Retardation, X-Linked \| ∟ Muscular Dystrophy, Duchenne \| ∟ Muscular Dystrophy, Emery-Dreifuss \| ∟ Oculocerebrorenal Syndrome \| ∟ Pelizaeus-Merzbacher Disease \| ∟ X-Linked Combined Immunodeficiency Diseases \| ∟ Activated Protein C Resistance \| ∟ Antithrombin III Deficiency \| ∟ Hermanski-Pudlak Syndrome \| ∟ Protein C Deficiency \| ∟ Purpura, Thrombotic Thrombocytopenic \| ∟ Agammaglobulinemia \| ∟ Ataxia Telangiectasia \| ∟ Common Variable Immunodeficiency \| ∟ Deltaretrovirus Infections \| ∟ DiGeorge Syndrome \| ∟ Dysgammaglobulinemia \| ∟ HIV Infections \| ∟ Leukocyte-Adhesion Deficiency Syndrome \| ∟ Lymphopenia \| ∟ Phagocyte Bactericidal Dysfunction \| ∟ Severe Combined Immunodeficiency Medical Subject Headings (MeSH) ∟ Immune System Diseases ∟ Purpura, Thrombocytopenic ∟ Wiskott-Aldrich Syndrome 54 coordinate concepts ∟ Afibrinogenemia \| ∟ Bernard-Soulier Syndrome \| ∟ Disseminated Intravascular Coagulation \| ∟ Factor V Deficiency \| ∟ Factor VII Deficiency \| ∟ Factor X Deficiency \| ∟ Factor XI Deficiency \| ∟ Factor XII Deficiency \| ∟ Factor XIII Deficiency \| ∟ Hemophilia A \| ∟ Hemophilia B \| ∟ Hypoprothrombinemias \| ∟ Platelet Storage Pool Deficiency \| ∟ Purpura, Thrombocytopenic, Idiopathic \| ∟ Thrombasthenia \| ∟ Thrombocythemia, Hemorrhagic \| ∟ Vascular Hemostatic Disorders \| ∟ Vitamin K Deficiency \| ∟ von Willebrand Disease \| ∟ Waterhouse-Friderichsen Syndrome \| ∟ Androgen-Insensitivity Syndrome \| ∟ Choroideremia \| ∟ Dyskeratosis Congenita \| ∟ Ectodermal Dysplasia 1, Anhidrotic \| ∟ Fabry Disease \| ∟ Focal Dermal Hypoplasia \| ∟ Glycogen Storage Disease Type IIb \| ∟ Glycogen Storage Disease Type VIII \| ∟ Granulomatous Disease, Chronic \| ∟ Hyper-IgM Immunodeficiency Syndrome, Type 1 \| ∟ Hypophosphatemic Rickets, X-Linked Dominant \| ∟ Ichthyosis, X-Linked \| ∟ Mental Retardation, X-Linked \| ∟ Muscular Dystrophy, Duchenne \| ∟ Muscular Dystrophy, Emery-Dreifuss \| ∟ Oculocerebrorenal Syndrome \| ∟ Pelizaeus-Merzbacher Disease \| ∟ X-Linked Combined Immunodeficiency Diseases \| ∟ Activated Protein C Resistance \| ∟ Antithrombin III Deficiency \| ∟ Hermanski-Pudlak Syndrome \| ∟ Protein C Deficiency \| ∟ Purpura, Thrombotic Thrombocytopenic \| ∟ Agammaglobulinemia \| ∟ Ataxia Telangiectasia \| ∟ Common Variable Immunodeficiency \| ∟ Deltaretrovirus Infections \| ∟ DiGeorge Syndrome \| ∟ Dysgammaglobulinemia \| ∟ HIV Infections \| ∟ Leukocyte-Adhesion Deficiency Syndrome \| ∟ Lymphopenia \| ∟ Phagocyte Bactericidal Dysfunction \| ∟ Severe Combined Immunodeficiency Medical Subject Headings (MeSH) ∟ Pathological Conditions, Signs and Symptoms ∟ Signs and Symptoms ∟ Skin Manifestations ∟ Purpura ∟ Purpura, Thrombocytopenic ∟ Wiskott-Aldrich Syndrome 54 coordinate concepts ∟ Afibrinogenemia \| ∟ Bernard-Soulier Syndrome \| ∟ Disseminated Intravascular Coagulation \| ∟ Factor V Deficiency \| ∟ Factor VII Deficiency \| ∟ Factor X Deficiency \| ∟ Factor XI Deficiency \| ∟ Factor XII Deficiency \| ∟ Factor XIII Deficiency \| ∟ Hemophilia A \| ∟ Hemophilia B \| ∟ Hypoprothrombinemias \| ∟ Platelet Storage Pool Deficiency \| ∟ Purpura, Thrombocytopenic, Idiopathic \| ∟ Thrombasthenia \| ∟ Thrombocythemia, Hemorrhagic \| ∟ Vascular Hemostatic Disorders \| ∟ Vitamin K Deficiency \| ∟ von Willebrand Disease \| ∟ Waterhouse-Friderichsen Syndrome \| ∟ Androgen-Insensitivity Syndrome \| ∟ Choroideremia \| ∟ Dyskeratosis Congenita \| ∟ Ectodermal Dysplasia 1, Anhidrotic \| ∟ Fabry Disease \| ∟ Focal Dermal Hypoplasia \| ∟ Glycogen Storage Disease Type IIb \| ∟ Glycogen Storage Disease Type VIII \| ∟ Granulomatous Disease, Chronic \| ∟ Hyper-IgM Immunodeficiency Syndrome, Type 1 \| ∟ Hypophosphatemic Rickets, X-Linked Dominant \| ∟ Ichthyosis, X-Linked \| ∟ Mental Retardation, X-Linked \| ∟ Muscular Dystrophy, Duchenne \| ∟ Muscular Dystrophy, Emery-Dreifuss \| ∟ Oculocerebrorenal Syndrome \| ∟ Pelizaeus-Merzbacher Disease \| ∟ X-Linked Combined Immunodeficiency Diseases \| ∟ Activated Protein C Resistance \| ∟ Antithrombin III Deficiency \| ∟ Hermanski-Pudlak Syndrome \| ∟ Protein C Deficiency \| ∟ Purpura, Thrombotic Thrombocytopenic \| ∟ Agammaglobulinemia \| ∟ Ataxia Telangiectasia \| ∟ Common Variable Immunodeficiency \| ∟ Deltaretrovirus Infections \| ∟ DiGeorge Syndrome \| ∟ Dysgammaglobulinemia \| ∟ HIV Infections \| ∟ Leukocyte-Adhesion Deficiency Syndrome \| ∟ Lymphopenia \| ∟ Phagocyte Bactericidal Dysfunction \| ∟ Severe Combined Immunodeficiency Medical Subject Headings (MeSH) ∟ Skin and Connective Tissue Diseases ∟ Skin Diseases ∟ Skin Manifestations ∟ Purpura ∟ Purpura, Thrombocytopenic ∟ Wiskott-Aldrich Syndrome 54 coordinate concepts ∟ Afibrinogenemia \| ∟ Bernard-Soulier Syndrome \| ∟ Disseminated Intravascular Coagulation \| ∟ Factor V Deficiency \| ∟ Factor VII Deficiency \| ∟ Factor X Deficiency \| ∟ Factor XI Deficiency \| ∟ Factor XII Deficiency \| ∟ Factor XIII Deficiency \| ∟ Hemophilia A \| ∟ Hemophilia B \| ∟ Hypoprothrombinemias \| ∟ Platelet Storage Pool Deficiency \| ∟ Purpura, Thrombocytopenic, Idiopathic \| ∟ Thrombasthenia \| ∟ Thrombocythemia, Hemorrhagic \| ∟ Vascular Hemostatic Disorders \| ∟ Vitamin K Deficiency \| ∟ von Willebrand Disease \| ∟ Waterhouse-Friderichsen Syndrome \| ∟ Androgen-Insensitivity Syndrome \| ∟ Choroideremia \| ∟ Dyskeratosis Congenita \| ∟ Ectodermal Dysplasia 1, Anhidrotic \| ∟ Fabry Disease \| ∟ Focal Dermal Hypoplasia \| ∟ Glycogen Storage Disease Type IIb \| ∟ Glycogen Storage Disease Type VIII \| ∟ Granulomatous Disease, Chronic \| ∟ Hyper-IgM Immunodeficiency Syndrome, Type 1 \| ∟ Hypophosphatemic Rickets, X-Linked Dominant \| ∟ Ichthyosis, X-Linked \| ∟ Mental Retardation, X-Linked \| ∟ Muscular Dystrophy, Duchenne \| ∟ Muscular Dystrophy, Emery-Dreifuss \| ∟ Oculocerebrorenal Syndrome \| ∟ Pelizaeus-Merzbacher Disease \| ∟ X-Linked Combined Immunodeficiency Diseases \| ∟ Activated Protein C Resistance \| ∟ Antithrombin III Deficiency \| ∟ Hermanski-Pudlak Syndrome \| ∟ Protein C Deficiency \| ∟ Purpura, Thrombotic Thrombocytopenic \| ∟ Agammaglobulinemia \| ∟ Ataxia Telangiectasia \| ∟ Common Variable Immunodeficiency \| ∟ Deltaretrovirus Infections \| ∟ DiGeorge Syndrome \| ∟ Dysgammaglobulinemia \| ∟ HIV Infections \| ∟ Leukocyte-Adhesion Deficiency Syndrome \| ∟ Lymphopenia \| ∟ Phagocyte Bactericidal Dysfunction \| ∟ Severe Combined Immunodeficiency X
Broader terms:	Medical Subject Headings (MeSH) ∟ Congenital, Hereditary, and Neonatal Diseases and Abnormalities ∟ Genetic Diseases, Inborn ∟ Blood Coagulation Disorders, Inherited ∟ Wiskott-Aldrich Syndrome Medical Subject Headings (MeSH) ∟ Congenital, Hereditary, and Neonatal Diseases and Abnormalities ∟ Genetic Diseases, Inborn ∟ Genetic Diseases, X-Linked ∟ Wiskott-Aldrich Syndrome Medical Subject Headings (MeSH) ∟ Hemic and Lymphatic Diseases ∟ Hematologic Diseases ∟ Blood Coagulation Disorders ∟ Blood Coagulation Disorders, Inherited ∟ Wiskott-Aldrich Syndrome Medical Subject Headings (MeSH) ∟ Hemic and Lymphatic Diseases ∟ Hematologic Diseases ∟ Blood Coagulation Disorders ∟ Purpura ∟ Purpura, Thrombocytopenic ∟ Wiskott-Aldrich Syndrome Medical Subject Headings (MeSH) ∟ Hemic and Lymphatic Diseases ∟ Hematologic Diseases ∟ Blood Coagulation Disorders ∟ Purpura, Thrombocytopenic ∟ Wiskott-Aldrich Syndrome Medical Subject Headings (MeSH) ∟ Hemic and Lymphatic Diseases ∟ Hematologic Diseases ∟ Blood Platelet Disorders ∟ Thrombocytopenia ∟ Purpura, Thrombocytopenic ∟ Wiskott-Aldrich Syndrome Medical Subject Headings (MeSH) ∟ Hemic and Lymphatic Diseases ∟ Hematologic Diseases ∟ Hemorrhagic Disorders ∟ Wiskott-Aldrich Syndrome Medical Subject Headings (MeSH) ∟ Immune System Diseases ∟ Immunologic Deficiency Syndromes ∟ Wiskott-Aldrich Syndrome Medical Subject Headings (MeSH) ∟ Immune System Diseases ∟ Purpura, Thrombocytopenic ∟ Wiskott-Aldrich Syndrome Medical Subject Headings (MeSH) ∟ Pathological Conditions, Signs and Symptoms ∟ Signs and Symptoms ∟ Skin Manifestations ∟ Purpura ∟ Purpura, Thrombocytopenic ∟ Wiskott-Aldrich Syndrome Medical Subject Headings (MeSH) ∟ Skin and Connective Tissue Diseases ∟ Skin Diseases ∟ Skin Manifestations ∟ Purpura ∟ Purpura, Thrombocytopenic ∟ Wiskott-Aldrich Syndrome Blood Coagulation Disorders, Inherited > Genetic Diseases, Inborn > Congenital, Hereditary, and Neonatal Diseases and Abnormalities > Medical Subject Headings (MeSH) Genetic Diseases, X-Linked > Genetic Diseases, Inborn > Congenital, Hereditary, and Neonatal Diseases and Abnormalities > Medical Subject Headings (MeSH) Blood Coagulation Disorders, Inherited > Blood Coagulation Disorders > Hematologic Diseases > Hemic and Lymphatic Diseases > Medical Subject Headings (MeSH) Purpura, Thrombocytopenic > Purpura > Blood Coagulation Disorders > Hematologic Diseases > Hemic and Lymphatic Diseases > Medical Subject Headings (MeSH) Purpura, Thrombocytopenic > Blood Coagulation Disorders > Hematologic Diseases > Hemic and Lymphatic Diseases > Medical Subject Headings (MeSH) Purpura, Thrombocytopenic > Thrombocytopenia > Blood Platelet Disorders > Hematologic Diseases > Hemic and Lymphatic Diseases > Medical Subject Headings (MeSH) Hemorrhagic Disorders > Hematologic Diseases > Hemic and Lymphatic Diseases > Medical Subject Headings (MeSH) Immunologic Deficiency Syndromes > Immune System Diseases > Medical Subject Headings (MeSH) Purpura, Thrombocytopenic > Immune System Diseases > Medical Subject Headings (MeSH) Purpura, Thrombocytopenic > Purpura > Skin Manifestations > Signs and Symptoms > Pathological Conditions, Signs and Symptoms > Medical Subject Headings (MeSH) Purpura, Thrombocytopenic > Purpura > Skin Manifestations > Skin Diseases > Skin and Connective Tissue Diseases > Medical Subject Headings (MeSH) X
historyNote*:	85; was ALDRICH SYNDROME 1963-84 X
onlineNote*:	use WISKOTT-ALDRICH SYNDROME to search ALDRICH SYNDROME 1966-84 X
publicMeSHNote*:	85; was ALDRICH SYNDROME 1963-84 X
Scope note:	A rare, X-linked immunodeficiency syndrome characterized by eczema, thrombocytopenic purpura, and recurrent pyogenic infection. It is seen exclusively in young boys. Typically, IMMUNOGLOBULIN M levels are low and IMMUNOGLOBULIN A and IMMUNOGLOBULIN E levels are elevated. Lymphoreticular malignancies are common. X
activeMeSHYear*:	2007X
dateCreated*:	1999-01-01X
dateRevised*:	2006-07-05X
recordAuthorizer*:	sjnX
recordMaintainer*:	agsX
recordOriginator*:	NLMX
Type:	Concept X
Coordinate terms:	Afibrinogenemia \| Bernard-Soulier Syndrome \| Disseminated Intravascular Coagulation \| Factor V Deficiency \| Factor VII Deficiency \| Factor X Deficiency \| Factor XI Deficiency \| Factor XII Deficiency \| Factor XIII Deficiency \| Hemophilia A \| Hemophilia B \| Hypoprothrombinemias \| Platelet Storage Pool Deficiency \| Purpura, Thrombocytopenic, Idiopathic \| Thrombasthenia \| Thrombocythemia, Hemorrhagic \| Vascular Hemostatic Disorders \| Vitamin K Deficiency \| von Willebrand Disease \| Waterhouse-Friderichsen Syndrome \| Androgen-Insensitivity Syndrome \| Choroideremia \| Dyskeratosis Congenita \| Ectodermal Dysplasia 1, Anhidrotic \| Fabry Disease \| Focal Dermal Hypoplasia \| Glycogen Storage Disease Type IIb \| Glycogen Storage Disease Type VIII \| Granulomatous Disease, Chronic \| Hyper-IgM Immunodeficiency Syndrome, Type 1 \| Hypophosphatemic Rickets, X-Linked Dominant \| Ichthyosis, X-Linked \| Mental Retardation, X-Linked \| Muscular Dystrophy, Duchenne \| Muscular Dystrophy, Emery-Dreifuss \| Oculocerebrorenal Syndrome \| Pelizaeus-Merzbacher Disease \| X-Linked Combined Immunodeficiency Diseases \| Activated Protein C Resistance \| Antithrombin III Deficiency \| Hermanski-Pudlak Syndrome \| Protein C Deficiency \| Purpura, Thrombotic Thrombocytopenic \| Agammaglobulinemia \| Ataxia Telangiectasia \| Common Variable Immunodeficiency \| Deltaretrovirus Infections \| DiGeorge Syndrome \| Dysgammaglobulinemia \| HIV Infections \| Leukocyte-Adhesion Deficiency Syndrome \| Lymphopenia \| Phagocyte Bactericidal Dysfunction \| Severe Combined Immunodeficiency X
URI:	X
Labels and equivalent concepts:	Wiskott-Aldrichin oireyhtymä (fi) Wiskott-Aldrichin syndrooma (fi, replaced) Wiskott-Aldrichs syndrom (sv) Aldrich Syndrome (en, replaced) Syndroma Wiskott-Aldrich (la-FI, replaced) X
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