ONKI3 | Medical Subject Headings

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Neoplastic Syndromes, Hereditary

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Hierarchy:	Medical Subject Headings (MeSH) ∟ Congenital, Hereditary, and Neonatal Diseases and Abnormalities ∟ Genetic Diseases, Inborn ∟ Neoplastic Syndromes, Hereditary 50 coordinate concepts 12 subordinate concepts ∟ Adenomatous Polyposis Coli \| ∟ Basal Cell Nevus Syndrome \| ∟ Colorectal Neoplasms, Hereditary Nonpolyposis \| ∟ Dysplastic Nevus Syndrome \| ∟ Exostoses, Multiple Hereditary \| ∟ Hamartoma Syndrome, Multiple \| ∟ Li-Fraumeni Syndrome \| ∟ Multiple Endocrine Neoplasia \| ∟ Neurofibromatoses \| ∟ Peutz-Jeghers Syndrome \| ∟ Sturge-Weber Syndrome \| ∟ Wilms Tumor ∟ Cysts \| ∟ D009369Q000556* \| ∟ Hamartoma \| ∟ Neoplasms by Histologic Type \| ∟ Neoplasms by Site \| ∟ Neoplasms, Experimental \| ∟ Neoplasms, Hormone-Dependent \| ∟ Neoplasms, Multiple Primary \| ∟ Neoplasms, Post-Traumatic \| ∟ Neoplasms, Radiation-Induced \| ∟ Neoplasms, Second Primary \| ∟ Neoplastic Processes \| ∟ Paraneoplastic Syndromes \| ∟ Precancerous Conditions \| ∟ Pregnancy Complications, Neoplastic \| ∟ Tumor Virus Infections \| ∟ Adrenal Hyperplasia, Congenital \| ∟ Anemia, Hemolytic, Congenital \| ∟ Anemia, Hypoplastic, Congenital \| ∟ Ataxia Telangiectasia \| ∟ Blood Coagulation Disorders, Inherited \| ∟ Brugada Syndrome \| ∟ CADASIL \| ∟ Camurati-Engelmann Syndrome \| ∟ Cardiomyopathy, Hypertrophic, Familial \| ∟ Cherubism \| ∟ Chromosome Disorders \| ∟ Cystic Fibrosis \| ∟ Dwarfism \| ∟ Eye Diseases, Hereditary \| ∟ Familial Mediterranean Fever \| ∟ Genetic Diseases, X-Linked \| ∟ Genetic Diseases, Y-Linked \| ∟ Hajdu-Cheney Syndrome \| ∟ Hemoglobinopathies \| ∟ Heredodegenerative Disorders, Nervous System \| ∟ Hyperthyroxinemia, Familial Dysalbuminemic \| ∟ Jervell-Lange Nielsen Syndrome \| ∟ Kallmann Syndrome \| ∟ Kartagener Syndrome \| ∟ Marfan Syndrome \| ∟ Metabolism, Inborn Errors \| ∟ Muscular Dystrophies \| ∟ Myasthenic Syndromes, Congenital \| ∟ Nail-Patella Syndrome \| ∟ Osteogenesis Imperfecta \| ∟ Pain Insensitivity, Congenital \| ∟ Romano-Ward Syndrome \| ∟ Skin Diseases, Genetic \| ∟ Werner Syndrome Medical Subject Headings (MeSH) ∟ Neoplasms ∟ Neoplastic Syndromes, Hereditary 50 coordinate concepts 12 subordinate concepts ∟ Adenomatous Polyposis Coli \| ∟ Basal Cell Nevus Syndrome \| ∟ Colorectal Neoplasms, Hereditary Nonpolyposis \| ∟ Dysplastic Nevus Syndrome \| ∟ Exostoses, Multiple Hereditary \| ∟ Hamartoma Syndrome, Multiple \| ∟ Li-Fraumeni Syndrome \| ∟ Multiple Endocrine Neoplasia \| ∟ Neurofibromatoses \| ∟ Peutz-Jeghers Syndrome \| ∟ Sturge-Weber Syndrome \| ∟ Wilms Tumor ∟ Cysts \| ∟ D009369Q000556* \| ∟ Hamartoma \| ∟ Neoplasms by Histologic Type \| ∟ Neoplasms by Site \| ∟ Neoplasms, Experimental \| ∟ Neoplasms, Hormone-Dependent \| ∟ Neoplasms, Multiple Primary \| ∟ Neoplasms, Post-Traumatic \| ∟ Neoplasms, Radiation-Induced \| ∟ Neoplasms, Second Primary \| ∟ Neoplastic Processes \| ∟ Paraneoplastic Syndromes \| ∟ Precancerous Conditions \| ∟ Pregnancy Complications, Neoplastic \| ∟ Tumor Virus Infections \| ∟ Adrenal Hyperplasia, Congenital \| ∟ Anemia, Hemolytic, Congenital \| ∟ Anemia, Hypoplastic, Congenital \| ∟ Ataxia Telangiectasia \| ∟ Blood Coagulation Disorders, Inherited \| ∟ Brugada Syndrome \| ∟ CADASIL \| ∟ Camurati-Engelmann Syndrome \| ∟ Cardiomyopathy, Hypertrophic, Familial \| ∟ Cherubism \| ∟ Chromosome Disorders \| ∟ Cystic Fibrosis \| ∟ Dwarfism \| ∟ Eye Diseases, Hereditary \| ∟ Familial Mediterranean Fever \| ∟ Genetic Diseases, X-Linked \| ∟ Genetic Diseases, Y-Linked \| ∟ Hajdu-Cheney Syndrome \| ∟ Hemoglobinopathies \| ∟ Heredodegenerative Disorders, Nervous System \| ∟ Hyperthyroxinemia, Familial Dysalbuminemic \| ∟ Jervell-Lange Nielsen Syndrome \| ∟ Kallmann Syndrome \| ∟ Kartagener Syndrome \| ∟ Marfan Syndrome \| ∟ Metabolism, Inborn Errors \| ∟ Muscular Dystrophies \| ∟ Myasthenic Syndromes, Congenital \| ∟ Nail-Patella Syndrome \| ∟ Osteogenesis Imperfecta \| ∟ Pain Insensitivity, Congenital \| ∟ Romano-Ward Syndrome \| ∟ Skin Diseases, Genetic \| ∟ Werner Syndrome X
Broader terms:	Medical Subject Headings (MeSH) ∟ Congenital, Hereditary, and Neonatal Diseases and Abnormalities ∟ Genetic Diseases, Inborn ∟ Neoplastic Syndromes, Hereditary Medical Subject Headings (MeSH) ∟ Neoplasms ∟ Neoplastic Syndromes, Hereditary Genetic Diseases, Inborn > Congenital, Hereditary, and Neonatal Diseases and Abnormalities > Medical Subject Headings (MeSH) Neoplasms > Medical Subject Headings (MeSH) X
Narrower terms:	Adenomatous Polyposis Coli \| Basal Cell Nevus Syndrome \| Colorectal Neoplasms, Hereditary Nonpolyposis \| Dysplastic Nevus Syndrome \| Exostoses, Multiple Hereditary \| Hamartoma Syndrome, Multiple \| Li-Fraumeni Syndrome \| Multiple Endocrine Neoplasia \| Neurofibromatoses \| Peutz-Jeghers Syndrome \| Sturge-Weber Syndrome \| Wilms Tumor X
Annotation:	do not use /blood supply /chem /second /secret /ultrastruct; coord IM with specific hereditary organ/neopl term (IM) or specific hereditary histol type (IM) X
historyNote*:	87 X
publicMeSHNote*:	87 X
Scope note:	The condition of a pattern of malignancies within a family, but not every individual's necessarily having the same neoplasm. Characteristically the tumor tends to occur at an earlier than average age, individuals may have more than one primary tumor, the tumors may be multicentric, usually more than 25 percent of the individuals in direct lineal descent from the proband are affected, and the cancer predisposition in these families behaves as an autosomal dominant trait with about 60 percent penetrance. X
activeMeSHYear*:	2002 \| 2003 \| 2004 \| 2005 \| 2006 \| 2007X
dateCreated*:	1986-06-23X
dateEstablished*:	1987-01-01X
dateRevised*:	2001-07-25X
recordAuthorizer*:	sjnX
recordMaintainer*:	nnsX
recordOriginator*:	VDKX
Type:	Concept X
Coordinate terms:	Cysts \| D009369Q000556* \| Hamartoma \| Neoplasms by Histologic Type \| Neoplasms by Site \| Neoplasms, Experimental \| Neoplasms, Hormone-Dependent \| Neoplasms, Multiple Primary \| Neoplasms, Post-Traumatic \| Neoplasms, Radiation-Induced \| Neoplasms, Second Primary \| Neoplastic Processes \| Paraneoplastic Syndromes \| Precancerous Conditions \| Pregnancy Complications, Neoplastic \| Tumor Virus Infections \| Adrenal Hyperplasia, Congenital \| Anemia, Hemolytic, Congenital \| Anemia, Hypoplastic, Congenital \| Ataxia Telangiectasia \| Blood Coagulation Disorders, Inherited \| Brugada Syndrome \| CADASIL \| Camurati-Engelmann Syndrome \| Cardiomyopathy, Hypertrophic, Familial \| Cherubism \| Chromosome Disorders \| Cystic Fibrosis \| Dwarfism \| Eye Diseases, Hereditary \| Familial Mediterranean Fever \| Genetic Diseases, X-Linked \| Genetic Diseases, Y-Linked \| Hajdu-Cheney Syndrome \| Hemoglobinopathies \| Heredodegenerative Disorders, Nervous System \| Hyperthyroxinemia, Familial Dysalbuminemic \| Jervell-Lange Nielsen Syndrome \| Kallmann Syndrome \| Kartagener Syndrome \| Marfan Syndrome \| Metabolism, Inborn Errors \| Muscular Dystrophies \| Myasthenic Syndromes, Congenital \| Nail-Patella Syndrome \| Osteogenesis Imperfecta \| Pain Insensitivity, Congenital \| Romano-Ward Syndrome \| Skin Diseases, Genetic \| Werner Syndrome X
URI:	X
Labels and equivalent concepts:	Perinnölliset neoplastiset oireyhtymät (fi) Periytyvät neoplastiset oireyhtymät (fi, replaced) Periytyvät neoplastiset syndroomat (fi, replaced) Perinnölliset neoplastiset syndroomat (fi, replaced) Hereditaariset neoplastiset syndroomat (fi, replaced) Hereditaariset neoplastiset oireyhtymät (fi, replaced) Neoplastiska syndrom, ärftliga (sv) Ärftliga neoplastiska syndrom (sv, replaced) Hereditary Cancer Syndromes (en, replaced) Hereditary Neoplastic Syndromes (en, replaced) Cancer Syndromes, Hereditary (en, replaced) X
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