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N-Acetylgalactosamine-4-Sulfatase
Hierarchy: | ∟ ∟ ∟ ∟ ∟ ∟ ∟ N-Acetylgalactosamine-4-Sulfatase 3 coordinate concepts1 subordinate concept∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ N-Acetylgalactosamine-4-Sulfatase 3 coordinate concepts1 subordinate concept∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ N-Acetylgalactosamine-4-Sulfatase 3 coordinate concepts1 subordinate conceptX |
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History note: | Sulfatases (1988-1998)X |
historyNote*: | 99; for ARYLSULFATASE B use CHONDRO-4-SULFATASE 1975-98; use N-ACETYLGALACTOSAMINE-4-SULFATASE (NM) 1988-98
X |
publicMeSHNote*: | 99; for ARYLSULFATASE B see CHONDRO-4-SULFATASE 1975-98; N-ACETYLGALACTOSAMINE-4-SULFATE SULFATASE (now N-ACETYLGALACTOSAMINE-4-SULFATASE) was indexed under SULFATASES 1988-98
X |
Scope note: | An arylsulfatase that catalyzes the hydrolysis of the 4-sulfate groups of the N-acetyl-D-galactosamine 4-sulfate units of chondroitin sulfate and dermatan sulfate. A deficiency of this enzyme is responsible for the inherited lysosomal disease, Maroteaux-Lamy syndrome (MUCOPOLYSACCHARIDOSIS VI). EC 3.1.6.12.
X |
activeMeSHYear*: | |
dateCreated*: | 1998-06-10X |
dateEstablished*: | 1999-01-01X |
dateRevised*: | 2003-07-09X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | ssbX |
recordOriginator*: | ADPX |
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Labels and equivalent concepts: | N-asetyyligalaktoosiamiini-4-sulfataasi (fi) XAryylisulfataasi B (fi, replaced) N-acetylgalaktosamin-4-sulfatas (sv) N-Acetylgalactosamine-4-sulphate Sulphatase (en, replaced) N-Acetylgalactosamine-4-sulfate Sulfatase (en, replaced) N-Acetylgalactosamine 4-Sulfatase (en, replaced) Arylsulfatase B (en, replaced) |
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