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1-Pyrroline-5-Carboxylate Dehydrogenase
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historyNote*: | 2006(1981)
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publicMeSHNote*: | 2006; 1-PYRROLINE-5-CARBOXYLATE DEHYDROGENASE was indexed under AMINE OXIDOREDUCTASES 1981-2004
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Scope note: | An enzyme that catalyzes the oxidation of 1-pyrroline-5-carboxylate to L-GLUTAMATE in the presence of NAD. Defects in the enzyme are the cause of hyperprolinemia II.
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activeMeSHYear*: | |
dateCreated*: | 2005-06-30X |
dateEstablished*: | 2006-01-01X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | AKEX |
recordOriginator*: | AKEX |
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Labels and equivalent concepts: | 1-pyrroliini-5-karboksylaattidehydrogenaasi (fi) XNADP+ Specific 8-Glutamate Semialdehyde Dehydrogenase (en, replaced) Glutamyl-Gamma-Semialdehyde Dehydrogenase (en, replaced) Glutamic-Gamma-Semialdehyde Dehydrogenase (en, replaced) GGS Dehydrogenase (en, replaced) Delta(1)-Pyrroline-5-Carboxylate Dehydrogenase (en, replaced) 1-Pirrolina-5-Carboxilato Deshidrogenasa (es) 1-Pyrrolin-5-Carboxylat-Dehydrogenase (de) 1-pyrrolin-5-karboxylátdehydrogenasa (cs) |
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