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The way concept relations are shown:
Severe Combined Immunodeficiency
Hierarchy: | ∟ ∟ ∟ Severe Combined Immunodeficiency 47 coordinate concepts1 subordinate concept∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Severe Combined Immunodeficiency 47 coordinate concepts1 subordinate concept∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Severe Combined Immunodeficiency 47 coordinate concepts1 subordinate concept∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ |
Broader terms: | ∟ ∟ ∟ Severe Combined Immunodeficiency ∟ ∟ ∟ Severe Combined Immunodeficiency ∟ ∟ ∟ ∟ Severe Combined Immunodeficiency |
Narrower terms: | |
History note: | Immunologic Deficiency Syndromes (1974-1991)X |
historyNote*: | 92
X |
publicMeSHNote*: | 92
X |
Scope note: | Group of rare congenital disorders characterized by impairment of both humoral and cell-mediated immunity, leukopenia, and low or absent antibody levels. It is inherited as an X-linked or autosomal recessive defect. Mutations occurring in many different genes cause human SCID.
X |
activeMeSHYear*: | |
dateCreated*: | 1991-01-03X |
dateEstablished*: | 1992-01-01X |
dateRevised*: | 2005-06-30X |
recordAuthorizer*: | sjnX |
recordMaintainer*: | nnsX |
recordOriginator*: | AGSX |
Type: | |
Coordinate terms: | |
URI: | |
Labels and equivalent concepts: | SCID-oireyhtymä (fi) XSevere Combined Immunodeficiency Syndrome (en, replaced) Severe Combined Immunologic Deficiency (en, replaced) SCID (en, replaced) Immunologic Deficiency, Severe Combined (en, replaced) Immunodeficiency Syndrome, Severe Combined (en, replaced) Immunodeficiency, Severe Combined (en, replaced) Inmunodeficiencia Combinada Severa (es) σοβαρή συνδυασμένη ανοσοανεπάρκεια (el) Schwerer kombinierter Immundefekt (de) imunodeficience kombinovaná těžká (cs) SCID (es, replaced) Síndrome del Linfocito Desnudo (es, replaced) Immuninsuffizienz, schwere kombinierte (de, replaced) SCID (de, replaced) Bare-Lymphocyte-Syndrom (de, replaced) |
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