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Motor Neuron Disease
Hierarchy: | ∟ ∟ ∟ Motor Neuron Disease 19 coordinate concepts4 subordinate concepts∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Motor Neuron Disease 19 coordinate concepts4 subordinate concepts∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ |
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Annotation: | GEN or unspecified; prefer specifics
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historyNote*: | 92
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publicMeSHNote*: | 92
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Scope note: | Diseases characterized by a selective degeneration of the motor neurons of the spinal cord, brainstem, or motor cortex. Clinical subtypes are distinguished by the major site of degeneration. In AMYOTROPHIC LATERAL SCLEROSIS there is involvement of upper, lower, and brainstem motor neurons. In progressive muscular atrophy and related syndromes (see MUSCULAR ATROPHY, SPINAL) the motor neurons in the spinal cord are primarily affected. With progressive bulbar palsy (BULBAR PALSY, PROGRESSIVE), the initial degeneration occurs in the brainstem. In primary lateral sclerosis, the cortical neurons are affected in isolation. (Adams et al., Principles of Neurology, 6th ed, p1089)
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activeMeSHYear*: | |
dateCreated*: | 1991-06-21X |
dateEstablished*: | 1992-01-01X |
dateRevised*: | 2004-07-28X |
recordAuthorizer*: | jlsX |
recordMaintainer*: | jlsX |
recordOriginator*: | AGSX |
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Labels and equivalent concepts: | Motoneuronisairaus (fi) XUpper Motor Neuron Disease (en, replaced) Secondary Motor Neuron Disease (en, replaced) Primary Lateral Sclerosis (en, replaced) Motor System Disease (en, replaced) Motor Neuron Disease, Familial (en, replaced) Lower Motor Neuron Disease (en, replaced) Enfermedad de la Neurona Motora (es) νόσος κινητικού νευρώνα (el) Motoneuronenkrankheit (de) degenerace motorických neuronů (cs) Enfermedad de la Neurona Motora Familiar (es, replaced) Enfermedad de la Neurona Motora Inferior (es, replaced) Enfermedad de la Neurona Motora Superior (es, replaced) Esclerosis Lateral (es, replaced) Enfermedad de las Células del Asta Anterior (es, replaced) Lateralsklerose (de, replaced) Krankheit der Vorderhornzelle (de, replaced) Motoneuronenkrankheit, obere (de, replaced) Motoneuronenkrankheit, untere (de, replaced) Familiäre Motoneuronenkrankheit (de, replaced) |
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