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Dandy-Walker Syndrome
Hierarchy: | ∟ ∟ ∟ ∟ Dandy-Walker Syndrome 15 coordinate concepts∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Dandy-Walker Syndrome 15 coordinate concepts∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Dandy-Walker Syndrome 15 coordinate concepts∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Dandy-Walker Syndrome 15 coordinate concepts∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Dandy-Walker Syndrome 15 coordinate concepts∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ Dandy-Walker Syndrome 15 coordinate concepts∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ ∟ |
Broader terms: | ∟ ∟ ∟ ∟ Dandy-Walker Syndrome ∟ ∟ ∟ ∟ Dandy-Walker Syndrome ∟ ∟ ∟ ∟ ∟ Dandy-Walker Syndrome ∟ ∟ ∟ ∟ ∟ Dandy-Walker Syndrome ∟ ∟ ∟ ∟ ∟ ∟ Dandy-Walker Syndrome ∟ ∟ ∟ Dandy-Walker Syndrome |
History note: | |
historyNote*: | 1991(1970)
X |
publicMeSHNote*: | 1991; see HYDROCEPHALUS 1970-1990
X |
Scope note: | A congenital abnormality of the central nervous system marked by failure of the midline structures of the cerebellum to develop, dilation of the fourth ventricle, and upward displacement of the transverse sinuses, tentorium, and torcula. Clinical features include occipital bossing, progressive head enlargement, bulging of anterior fontanelle, papilledema, ataxia, gait disturbances, nystagmus, and intellectual compromise. (From Menkes, Textbook of Child Neurology, 5th ed, pp294-5)
X |
activeMeSHYear*: | |
dateCreated*: | 1999-01-01X |
dateEstablished*: | 1991-01-01X |
dateRevised*: | 1999-12-02X |
recordAuthorizer*: | agsX |
recordMaintainer*: | agsX |
recordOriginator*: | NLMX |
Type: | |
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Labels and equivalent concepts: | Dandy-Walkerin epämuodostuma (fi) XDandy-Walker Syndrome, Familial (en, replaced) Dandy-Walker Malformation (en, replaced) Síndrome de Dandy-Walker (es) σύνδρομο Dandy-Walker (el) Dandy-Walker-Syndrom (de) Dandyův-Walkerův syndrom (cs) Malformación de Dandy-Walker (es, replaced) Dandy-Walker-Fehlbildung (de, replaced) |
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