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beta-N-Acetylhexosaminidase
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Annotation: | do not confuse with ACETYLGLUCOSAMINIDASE; /defic: consider also TAY SACHS DISEASE and SANDHOFF DISEASE; coord with ISOENZYMES if discussed
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historyNote*: | 87
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publicMeSHNote*: | 87
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Scope note: | An enzyme hydrolyzing terminal non-reducing N-acetyl-D-hexosamine residues in N-acetyl-beta-D-hexosaminides. It acts on GLUCOSIDES; GALACTOSIDES; and several OLIGOSACCHARIDES. Hexosaminidase A cleaves GM2, GA2, globosides, and hexosamine oligosaccharides. Hexosaminidase B cleaves all the above substrates except GM2. Deficiency of Hexosaminidase A causes TAY-SACHS DISEASE, while deficiency of both A and B isozymes causes SANDHOFF DISEASE. The enzyme has also been used as a tumor marker to distinguish between malignant and benign disease.
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activeMeSHYear*: | |
dateCreated*: | 1986-06-02X |
dateEstablished*: | 1987-01-01X |
dateRevised*: | 2005-07-15X |
recordAuthorizer*: | agsX |
recordMaintainer*: | agsX |
recordOriginator*: | RLSX |
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Labels and equivalent concepts: | Beeta-N-asetyyliheksoaminidaasi (fi) XN-Acetyl-beta-D-hexosaminidase (en, replaced) Hex B (en, replaced) Hex A (en, replaced) beta-N-Acetylhexosaminidase A (en, replaced) beta-N-Acetyl-hexosaminidase (en, replaced) beta-N-Acetyl-D-hexosaminidase (en, replaced) beta-Hexosaminidase (en, replaced) beta-N-Acetilhexosaminidasa (es) βητα-Ν-ακετυλεξοζαμινιδάση (el) beta-N-acetylhexosaminidasa (cs) betahexosaminidasa (es, replaced) Hex A (es, replaced) Hexosaminidasa B (es, replaced) Hexosaminidasa A (es, replaced) Hex B (es, replaced) Hexosaminidase (de, replaced) Hex B (de, replaced) Hex A (de, replaced) Hexosaminidase A (de, replaced) Hexosaminidase B (de, replaced) Hexosaminidase-Isozyme (de, replaced) Hexosaminidase-Isoenzyme (de, replaced) Beta-Hexosaminidase (de, replaced) |
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